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Definitions and outcome measures for mucous membrane pemphigoid: recommendations of an international panel of experts.

Identifieur interne : 002F53 ( Main/Exploration ); précédent : 002F52; suivant : 002F54

Definitions and outcome measures for mucous membrane pemphigoid: recommendations of an international panel of experts.

Auteurs : Dedee F. Murrell [Australie] ; Branka Marinovic [Croatie] ; Frederic Caux [France] ; Catherine Prost [France] ; Razzaque Ahmed [États-Unis] ; Katarzyna Wozniak [Pologne] ; Masayuki Amagai [Japon] ; Johann Bauer [Autriche] ; Stefan Beissert [Allemagne] ; Luca Borradori [Suisse] ; Donna Culton [États-Unis] ; Janet A. Fairley [États-Unis] ; David Fivenson [États-Unis] ; Marcel F. Jonkman [Pays-Bas] ; M Peter Marinkovich [États-Unis] ; David Woodley [États-Unis] ; John Zone [États-Unis] ; Valeria Aoki [Brésil] ; Philippe Bernard [France] ; Leena Bruckner-Tuderman [Allemagne] ; Giuseppe Cianchini [Italie] ; Vanessa Venning [Royaume-Uni] ; Luis Diaz [États-Unis] ; Rudiger Eming [Allemagne] ; Sergei A. Grando [États-Unis] ; Russell P. Hall [États-Unis] ; Takashi Hashimoto [Japon] ; Josep E. Herrero-González [Espagne] ; Michael Hertl [Allemagne] ; Pascal Joly [France] ; Sarolta Karpati [Hongrie] ; Jaehwan Kim [États-Unis] ; Soo Chan Kim [Corée du Sud] ; Neil J. Korman [États-Unis] ; Cezary Kowalewski [Pologne] ; Sang Eun Lee [Corée du Sud] ; David R. Rubenstein [États-Unis] ; Eli Sprecher [Israël] ; Kim Yancey [États-Unis] ; Giovanna Zambruno [Italie] ; Detlef Zillikens [Allemagne] ; Serge Doan [France] ; Benjamin S. Daniel [Australie] ; Victoria P. Werth [États-Unis]

Source :

RBID : pubmed:25443626

Descripteurs français

English descriptors

Abstract

Mucous membrane pemphigoid encompasses a group of autoimmune bullous diseases with a similar phenotype characterized by subepithelial blisters, erosions, and scarring of mucous membranes, skin, or both. Although knowledge about autoimmune bullous disease is increasing, there is often a lack of clear definitions of disease, outcome measures, and therapeutic end points. With clearer definitions and outcome measures, it is possible to directly compare the results and data from various studies using meta-analyses. This consensus statement provides accurate and reproducible definitions for disease extent, activity, outcome measures, end points, and therapeutic response for mucous membrane pemphigoid and proposes a disease extent score, the Mucous Membrane Pemphigoid Disease Area Index.

DOI: 10.1016/j.jaad.2014.08.024
PubMed: 25443626


Affiliations:


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Le document en format XML

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<name sortKey="Zone, John" sort="Zone, John" uniqKey="Zone J" first="John" last="Zone">John Zone</name>
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<nlm:affiliation>Department of Dermatology, Reims University Hospital, University of Champagne-Ardenne, Reims, France.</nlm:affiliation>
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<nlm:affiliation>Department of Immunodermatology, Istituto Dermopatico dell'Immacolata, IRCCS, Rome, Italy; Laboratory of Molecular and Cell Biology, Istituto Dermopatico dell'Immacolata, IRCCS, Rome, Italy.</nlm:affiliation>
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<nlm:affiliation>Department of Dermatology, University of California, Irvine, California; Department of Biological Chemistry Cancer Center, University of California, Irvine, California; Research Institute, Institute for Immunology, University of California, Irvine, California.</nlm:affiliation>
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<nlm:affiliation>Kurume University School of Medicine, Kurume, Japan.</nlm:affiliation>
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<name sortKey="Herrero Gonzalez, Josep E" sort="Herrero Gonzalez, Josep E" uniqKey="Herrero Gonzalez J" first="Josep E" last="Herrero-González">Josep E. Herrero-González</name>
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<nlm:affiliation>Department of Dermatology, University Hospital, Marburg, Germany.</nlm:affiliation>
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<nlm:affiliation>Clinique Dermatologique, Institut National de la Sante et de la Recherche Medicale (INSERM), INSERM U905, Rouen University Hospital, University of Rouen, Rouen, France; Dermatology Department, Rouen University Hospital, University of Rouen, Rouen, France.</nlm:affiliation>
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<nlm:affiliation>Department of Dermatology, Venereology, and Dermatooncology of the Semmelweis University, Budapest, Hungary.</nlm:affiliation>
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<wicri:regionArea>Department of Dermatology, Venereology, and Dermatooncology of the Semmelweis University, Budapest</wicri:regionArea>
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<settlement type="city">Budapest</settlement>
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<name sortKey="Kim, Jaehwan" sort="Kim, Jaehwan" uniqKey="Kim J" first="Jaehwan" last="Kim">Jaehwan Kim</name>
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<nlm:affiliation>Department of Dermatology at St George Hospital, University of New South Wales, Sydney, Australia; Laboratory for Investigative Dermatology, Rockefeller University, New York, New York.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">État de New York</region>
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<wicri:cityArea>Department of Dermatology at St George Hospital, University of New South Wales, Sydney, Australia; Laboratory for Investigative Dermatology, Rockefeller University, New York</wicri:cityArea>
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<author>
<name sortKey="Chan Kim, Soo" sort="Chan Kim, Soo" uniqKey="Chan Kim S" first="Soo" last="Chan Kim">Soo Chan Kim</name>
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<nlm:affiliation>Department of Dermatology and Cutaneous Biology Research Institute, Yonsei University College of Medicine, Gangnam Severance Hospital, Seoul, Korea.</nlm:affiliation>
<country xml:lang="fr">Corée du Sud</country>
<wicri:regionArea>Department of Dermatology and Cutaneous Biology Research Institute, Yonsei University College of Medicine, Gangnam Severance Hospital, Seoul</wicri:regionArea>
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<settlement type="city">Séoul</settlement>
<region type="capital">Région capitale de Séoul</region>
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<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Ohio</region>
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</affiliation>
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<name sortKey="Kowalewski, Cezary" sort="Kowalewski, Cezary" uniqKey="Kowalewski C" first="Cezary" last="Kowalewski">Cezary Kowalewski</name>
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<nlm:affiliation>Department of Dermatology and Immunodermatology, Medical University of Warsaw, Warsaw, Poland.</nlm:affiliation>
<country xml:lang="fr">Pologne</country>
<wicri:regionArea>Department of Dermatology and Immunodermatology, Medical University of Warsaw, Warsaw</wicri:regionArea>
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<name sortKey="Lee, Sang Eun" sort="Lee, Sang Eun" uniqKey="Lee S" first="Sang Eun" last="Lee">Sang Eun Lee</name>
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<nlm:affiliation>Department of Dermatology, CHA Bundang Medical Center, CHA University, Seongnam, Korea.</nlm:affiliation>
<country xml:lang="fr">Corée du Sud</country>
<wicri:regionArea>Department of Dermatology, CHA Bundang Medical Center, CHA University, Seongnam</wicri:regionArea>
<wicri:noRegion>Seongnam</wicri:noRegion>
</affiliation>
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<name sortKey="Rubenstein, David R" sort="Rubenstein, David R" uniqKey="Rubenstein D" first="David R" last="Rubenstein">David R. Rubenstein</name>
<affiliation wicri:level="2">
<nlm:affiliation>Department of Dermatology, University of North Carolina at Chapel Hill, Chapel Hill, North Carolina.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Caroline du Nord</region>
</placeName>
<wicri:cityArea>Department of Dermatology, University of North Carolina at Chapel Hill, Chapel Hill</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Sprecher, Eli" sort="Sprecher, Eli" uniqKey="Sprecher E" first="Eli" last="Sprecher">Eli Sprecher</name>
<affiliation wicri:level="1">
<nlm:affiliation>Department of Dermatology, Tel Aviv Sourasky Medical Center, Tel Aviv, Israel.</nlm:affiliation>
<country xml:lang="fr">Israël</country>
<wicri:regionArea>Department of Dermatology, Tel Aviv Sourasky Medical Center, Tel Aviv</wicri:regionArea>
<wicri:noRegion>Tel Aviv</wicri:noRegion>
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<name sortKey="Yancey, Kim" sort="Yancey, Kim" uniqKey="Yancey K" first="Kim" last="Yancey">Kim Yancey</name>
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<nlm:affiliation>Department of Dermatology, University of Texas Southwestern Medical Center, Dallas, Texas.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Texas</region>
</placeName>
<wicri:cityArea>Department of Dermatology, University of Texas Southwestern Medical Center, Dallas</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Zambruno, Giovanna" sort="Zambruno, Giovanna" uniqKey="Zambruno G" first="Giovanna" last="Zambruno">Giovanna Zambruno</name>
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<nlm:affiliation>Laboratory of Molecular and Cell Biology, Istituto Dermopatico dell'Immacolata, IRCCS, Rome, Italy.</nlm:affiliation>
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Laboratory of Molecular and Cell Biology, Istituto Dermopatico dell'Immacolata, IRCCS, Rome</wicri:regionArea>
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<settlement type="city">Rome</settlement>
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<name sortKey="Zillikens, Detlef" sort="Zillikens, Detlef" uniqKey="Zillikens D" first="Detlef" last="Zillikens">Detlef Zillikens</name>
<affiliation wicri:level="1">
<nlm:affiliation>Department of Dermatology, University of Lubeck, Lubeck, Germany.</nlm:affiliation>
<country xml:lang="fr">Allemagne</country>
<wicri:regionArea>Department of Dermatology, University of Lubeck, Lubeck</wicri:regionArea>
<wicri:noRegion>Lubeck</wicri:noRegion>
<wicri:noRegion>Lubeck</wicri:noRegion>
<wicri:noRegion>Lubeck</wicri:noRegion>
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<name sortKey="Doan, Serge" sort="Doan, Serge" uniqKey="Doan S" first="Serge" last="Doan">Serge Doan</name>
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<nlm:affiliation>Department of Ophthalmology, Hopital Bichat, Paris, France; Fondation A de Rothschild, Paris, France.</nlm:affiliation>
<country xml:lang="fr">France</country>
<wicri:regionArea>Department of Ophthalmology, Hopital Bichat, Paris, France; Fondation A de Rothschild, Paris</wicri:regionArea>
<placeName>
<region type="region">Île-de-France</region>
<region type="old region">Île-de-France</region>
<settlement type="city">Paris</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Daniel, Benjamin S" sort="Daniel, Benjamin S" uniqKey="Daniel B" first="Benjamin S" last="Daniel">Benjamin S. Daniel</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology at St George Hospital, University of New South Wales, Sydney, Australia.</nlm:affiliation>
<country xml:lang="fr">Australie</country>
<wicri:regionArea>Department of Dermatology at St George Hospital, University of New South Wales, Sydney</wicri:regionArea>
<placeName>
<settlement type="city">Sydney</settlement>
<region type="état">Nouvelle-Galles du Sud</region>
</placeName>
</affiliation>
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<affiliation wicri:level="2">
<nlm:affiliation>Philadelphia Department of Veterans Affairs Medical Center, University of Pennsylvania, Philadelphia, Pennsylvania; Department of Dermatology, University of Pennsylvania, Philadelphia, Pennsylvania.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Pennsylvanie</region>
</placeName>
<wicri:cityArea>Philadelphia Department of Veterans Affairs Medical Center, University of Pennsylvania, Philadelphia, Pennsylvania; Department of Dermatology, University of Pennsylvania, Philadelphia</wicri:cityArea>
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<title xml:lang="en">Definitions and outcome measures for mucous membrane pemphigoid: recommendations of an international panel of experts.</title>
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<name sortKey="Murrell, Dedee F" sort="Murrell, Dedee F" uniqKey="Murrell D" first="Dedee F" last="Murrell">Dedee F. Murrell</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology at St George Hospital, University of New South Wales, Sydney, Australia. Electronic address: d.murrell@unsw.edu.au.</nlm:affiliation>
<country xml:lang="fr">Australie</country>
<wicri:regionArea>Department of Dermatology at St George Hospital, University of New South Wales, Sydney</wicri:regionArea>
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<settlement type="city">Sydney</settlement>
<region type="état">Nouvelle-Galles du Sud</region>
</placeName>
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<name sortKey="Marinovic, Branka" sort="Marinovic, Branka" uniqKey="Marinovic B" first="Branka" last="Marinovic">Branka Marinovic</name>
<affiliation wicri:level="1">
<nlm:affiliation>Department of Dermatology and Venereology, Zagreb University Hospital Center and School of Medicine, Zagreb, Croatia.</nlm:affiliation>
<country xml:lang="fr">Croatie</country>
<wicri:regionArea>Department of Dermatology and Venereology, Zagreb University Hospital Center and School of Medicine, Zagreb</wicri:regionArea>
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</affiliation>
</author>
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<name sortKey="Caux, Frederic" sort="Caux, Frederic" uniqKey="Caux F" first="Frederic" last="Caux">Frederic Caux</name>
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<nlm:affiliation>Department of Dermatology, Avicenne Hospital, University Paris 13, Bobigny, France.</nlm:affiliation>
<country xml:lang="fr">France</country>
<wicri:regionArea>Department of Dermatology, Avicenne Hospital, University Paris 13, Bobigny</wicri:regionArea>
<placeName>
<region type="region">Île-de-France</region>
<region type="old region">Île-de-France</region>
<settlement type="city">Bobigny</settlement>
</placeName>
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<name sortKey="Prost, Catherine" sort="Prost, Catherine" uniqKey="Prost C" first="Catherine" last="Prost">Catherine Prost</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology, Department of Histology, Reference Center for Autoimmune Bullous Diseases, Avicenne Hospital, University Paris 13, Bobigny, France.</nlm:affiliation>
<country xml:lang="fr">France</country>
<wicri:regionArea>Department of Dermatology, Department of Histology, Reference Center for Autoimmune Bullous Diseases, Avicenne Hospital, University Paris 13, Bobigny</wicri:regionArea>
<placeName>
<region type="region">Île-de-France</region>
<region type="old region">Île-de-France</region>
<settlement type="city">Bobigny</settlement>
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</author>
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<name sortKey="Ahmed, Razzaque" sort="Ahmed, Razzaque" uniqKey="Ahmed R" first="Razzaque" last="Ahmed">Razzaque Ahmed</name>
<affiliation wicri:level="2">
<nlm:affiliation>Center For Blistering Diseases, Boston, Massachusetts.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Massachusetts</region>
</placeName>
<wicri:cityArea>Center For Blistering Diseases, Boston</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Wozniak, Katarzyna" sort="Wozniak, Katarzyna" uniqKey="Wozniak K" first="Katarzyna" last="Wozniak">Katarzyna Wozniak</name>
<affiliation wicri:level="1">
<nlm:affiliation>Department of Dermatology and Immunodermatology, Medical University of Warsaw, Warsaw, Poland.</nlm:affiliation>
<country xml:lang="fr">Pologne</country>
<wicri:regionArea>Department of Dermatology and Immunodermatology, Medical University of Warsaw, Warsaw</wicri:regionArea>
<wicri:noRegion>Warsaw</wicri:noRegion>
</affiliation>
</author>
<author>
<name sortKey="Amagai, Masayuki" sort="Amagai, Masayuki" uniqKey="Amagai M" first="Masayuki" last="Amagai">Masayuki Amagai</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology, Keio University School of Medicine, Tokyo, Japan.</nlm:affiliation>
<country xml:lang="fr">Japon</country>
<wicri:regionArea>Department of Dermatology, Keio University School of Medicine, Tokyo</wicri:regionArea>
<placeName>
<settlement type="city">Tokyo</settlement>
<region type="région">Région de Kantō</region>
</placeName>
</affiliation>
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<name sortKey="Bauer, Johann" sort="Bauer, Johann" uniqKey="Bauer J" first="Johann" last="Bauer">Johann Bauer</name>
<affiliation wicri:level="1">
<nlm:affiliation>Division of Molecular Dermatology, Department of Dermatology, Paracelsus Medical University Salzburg, Salzburg, Austria.</nlm:affiliation>
<country xml:lang="fr">Autriche</country>
<wicri:regionArea>Division of Molecular Dermatology, Department of Dermatology, Paracelsus Medical University Salzburg, Salzburg</wicri:regionArea>
<wicri:noRegion>Salzburg</wicri:noRegion>
</affiliation>
</author>
<author>
<name sortKey="Beissert, Stefan" sort="Beissert, Stefan" uniqKey="Beissert S" first="Stefan" last="Beissert">Stefan Beissert</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology, University of Dresden, Dresden, Germany.</nlm:affiliation>
<country xml:lang="fr">Allemagne</country>
<wicri:regionArea>Department of Dermatology, University of Dresden, Dresden</wicri:regionArea>
<placeName>
<region type="land" nuts="1">Saxe (Land)</region>
<region type="district" nuts="2">District de Dresde</region>
<settlement type="city">Dresde</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Borradori, Luca" sort="Borradori, Luca" uniqKey="Borradori L" first="Luca" last="Borradori">Luca Borradori</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology, University Hospital of Bern, Bern, Switzerland.</nlm:affiliation>
<country xml:lang="fr">Suisse</country>
<wicri:regionArea>Department of Dermatology, University Hospital of Bern, Bern</wicri:regionArea>
<placeName>
<settlement type="city">Berne</settlement>
<region type="région" nuts="3">Canton de Berne</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Culton, Donna" sort="Culton, Donna" uniqKey="Culton D" first="Donna" last="Culton">Donna Culton</name>
<affiliation wicri:level="2">
<nlm:affiliation>Department of Dermatology, University of North Carolina at Chapel Hill, Chapel Hill, North Carolina.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Caroline du Nord</region>
</placeName>
<wicri:cityArea>Department of Dermatology, University of North Carolina at Chapel Hill, Chapel Hill</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Fairley, Janet A" sort="Fairley, Janet A" uniqKey="Fairley J" first="Janet A" last="Fairley">Janet A. Fairley</name>
<affiliation wicri:level="2">
<nlm:affiliation>Department of Dermatology, University of Iowa, Iowa City, Iowa; Department of Veterans Affairs Medical Center, Iowa City, Iowa.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Iowa</region>
</placeName>
<wicri:cityArea>Department of Dermatology, University of Iowa, Iowa City, Iowa; Department of Veterans Affairs Medical Center, Iowa City</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Fivenson, David" sort="Fivenson, David" uniqKey="Fivenson D" first="David" last="Fivenson">David Fivenson</name>
<affiliation wicri:level="2">
<nlm:affiliation>St Joseph Mercy Health System, Department of Dermatology, Ann Arbor, Michigan.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Michigan</region>
</placeName>
<wicri:cityArea>St Joseph Mercy Health System, Department of Dermatology, Ann Arbor</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Jonkman, Marcel F" sort="Jonkman, Marcel F" uniqKey="Jonkman M" first="Marcel F" last="Jonkman">Marcel F. Jonkman</name>
<affiliation wicri:level="3">
<nlm:affiliation>University Medical Center Groningen, University of Groningen, Groningen, The Netherlands.</nlm:affiliation>
<country xml:lang="fr">Pays-Bas</country>
<wicri:regionArea>University Medical Center Groningen, University of Groningen, Groningen</wicri:regionArea>
<placeName>
<settlement type="city">Groningue</settlement>
<region nuts="2" type="province">Groningue (province)</region>
</placeName>
</affiliation>
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<author>
<name sortKey="Marinkovich, M Peter" sort="Marinkovich, M Peter" uniqKey="Marinkovich M" first="M Peter" last="Marinkovich">M Peter Marinkovich</name>
<affiliation wicri:level="2">
<nlm:affiliation>Department of Dermatology, Stanford University School of Medicine, Stanford, California; Center for Clinical Sciences Research, and Division of Dermatology, Department of Veterans Affairs Palo Alto Healthcare System, Palo Alto, California.</nlm:affiliation>
<country>États-Unis</country>
<placeName>
<region type="state">Californie</region>
</placeName>
<wicri:cityArea>Department of Dermatology, Stanford University School of Medicine, Stanford, California; Center for Clinical Sciences Research, and Division of Dermatology, Department of Veterans Affairs Palo Alto Healthcare System, Palo Alto</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Woodley, David" sort="Woodley, David" uniqKey="Woodley D" first="David" last="Woodley">David Woodley</name>
<affiliation wicri:level="2">
<nlm:affiliation>Department of Dermatology, Keck School of Medicine, University of Southern California, Los Angeles, California.</nlm:affiliation>
<country>États-Unis</country>
<placeName>
<region type="state">Californie</region>
</placeName>
<wicri:cityArea>Department of Dermatology, Keck School of Medicine, University of Southern California, Los Angeles</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Zone, John" sort="Zone, John" uniqKey="Zone J" first="John" last="Zone">John Zone</name>
<affiliation wicri:level="2">
<nlm:affiliation>Department of Dermatology, School of Medicine, University of Utah, Salt Lake City, Utah.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Utah</region>
</placeName>
<wicri:cityArea>Department of Dermatology, School of Medicine, University of Utah, Salt Lake City</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Aoki, Valeria" sort="Aoki, Valeria" uniqKey="Aoki V" first="Valeria" last="Aoki">Valeria Aoki</name>
<affiliation wicri:level="4">
<nlm:affiliation>Department of Dermatology, University of Sao Paulo, Sao Paulo, Brazil.</nlm:affiliation>
<country xml:lang="fr">Brésil</country>
<wicri:regionArea>Department of Dermatology, University of Sao Paulo, Sao Paulo</wicri:regionArea>
<placeName>
<settlement type="city">São Paulo</settlement>
<region type="state">État de São Paulo</region>
<settlement type="city">São Paulo</settlement>
</placeName>
<orgName type="university">Université de São Paulo</orgName>
</affiliation>
</author>
<author>
<name sortKey="Bernard, Philippe" sort="Bernard, Philippe" uniqKey="Bernard P" first="Philippe" last="Bernard">Philippe Bernard</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology, Reims University Hospital, University of Champagne-Ardenne, Reims, France.</nlm:affiliation>
<country xml:lang="fr">France</country>
<wicri:regionArea>Department of Dermatology, Reims University Hospital, University of Champagne-Ardenne, Reims</wicri:regionArea>
<placeName>
<region type="region">Grand Est</region>
<region type="old region">Champagne-Ardenne</region>
<settlement type="city">Reims</settlement>
</placeName>
</affiliation>
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<author>
<name sortKey="Bruckner Tuderman, Leena" sort="Bruckner Tuderman, Leena" uniqKey="Bruckner Tuderman L" first="Leena" last="Bruckner-Tuderman">Leena Bruckner-Tuderman</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology, University Freiburg Medical Center, Freiburg, Germany.</nlm:affiliation>
<country xml:lang="fr">Allemagne</country>
<wicri:regionArea>Department of Dermatology, University Freiburg Medical Center, Freiburg</wicri:regionArea>
<placeName>
<region type="land" nuts="1">Bade-Wurtemberg</region>
<region type="district" nuts="2">District de Fribourg-en-Brisgau</region>
<settlement type="city">Fribourg-en-Brisgau</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Cianchini, Giuseppe" sort="Cianchini, Giuseppe" uniqKey="Cianchini G" first="Giuseppe" last="Cianchini">Giuseppe Cianchini</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Immunodermatology, Istituto Dermopatico dell'Immacolata, IRCCS, Rome, Italy; Laboratory of Molecular and Cell Biology, Istituto Dermopatico dell'Immacolata, IRCCS, Rome, Italy.</nlm:affiliation>
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Department of Immunodermatology, Istituto Dermopatico dell'Immacolata, IRCCS, Rome, Italy; Laboratory of Molecular and Cell Biology, Istituto Dermopatico dell'Immacolata, IRCCS, Rome</wicri:regionArea>
<placeName>
<settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Venning, Vanessa" sort="Venning, Vanessa" uniqKey="Venning V" first="Vanessa" last="Venning">Vanessa Venning</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology, Churchill Hospital, Oxford, United Kingdom.</nlm:affiliation>
<country xml:lang="fr">Royaume-Uni</country>
<wicri:regionArea>Department of Dermatology, Churchill Hospital, Oxford</wicri:regionArea>
<placeName>
<settlement type="city">Oxford</settlement>
<region type="country">Angleterre</region>
<region type="comté" nuts="2">Oxfordshire</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Diaz, Luis" sort="Diaz, Luis" uniqKey="Diaz L" first="Luis" last="Diaz">Luis Diaz</name>
<affiliation wicri:level="2">
<nlm:affiliation>Department of Dermatology, University of North Carolina at Chapel Hill, Chapel Hill, North Carolina.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Caroline du Nord</region>
</placeName>
<wicri:cityArea>Department of Dermatology, University of North Carolina at Chapel Hill, Chapel Hill</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Eming, Rudiger" sort="Eming, Rudiger" uniqKey="Eming R" first="Rudiger" last="Eming">Rudiger Eming</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology and Allergology, University Hospital, Philipps-Universität Marburg, Marburg, Germany.</nlm:affiliation>
<country xml:lang="fr">Allemagne</country>
<wicri:regionArea>Department of Dermatology and Allergology, University Hospital, Philipps-Universität Marburg, Marburg</wicri:regionArea>
<placeName>
<region type="land" nuts="1">Hesse (Land)</region>
<region type="district" nuts="2">District de Giessen</region>
<settlement type="city">Marbourg</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Grando, Sergei A" sort="Grando, Sergei A" uniqKey="Grando S" first="Sergei A" last="Grando">Sergei A. Grando</name>
<affiliation wicri:level="2">
<nlm:affiliation>Department of Dermatology, University of California, Irvine, California; Department of Biological Chemistry Cancer Center, University of California, Irvine, California; Research Institute, Institute for Immunology, University of California, Irvine, California.</nlm:affiliation>
<country>États-Unis</country>
<placeName>
<region type="state">Californie</region>
</placeName>
<wicri:cityArea>Department of Dermatology, University of California, Irvine, California; Department of Biological Chemistry Cancer Center, University of California, Irvine, California; Research Institute, Institute for Immunology, University of California, Irvine</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Hall, Russell P" sort="Hall, Russell P" uniqKey="Hall R" first="Russell P" last="Hall">Russell P. Hall</name>
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<country xml:lang="fr">États-Unis</country>
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<region type="state">Caroline du Nord</region>
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<wicri:cityArea>Division of Dermatology, Duke Medical Center, Durham</wicri:cityArea>
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<author>
<name sortKey="Hashimoto, Takashi" sort="Hashimoto, Takashi" uniqKey="Hashimoto T" first="Takashi" last="Hashimoto">Takashi Hashimoto</name>
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<nlm:affiliation>Kurume University School of Medicine, Kurume, Japan.</nlm:affiliation>
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<name sortKey="Herrero Gonzalez, Josep E" sort="Herrero Gonzalez, Josep E" uniqKey="Herrero Gonzalez J" first="Josep E" last="Herrero-González">Josep E. Herrero-González</name>
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<nlm:affiliation>Department of Dermatology, Hospital del Mar, Institut Hospital del Mar d'Investigacions Mèdiques, Barcelona, Spain.</nlm:affiliation>
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<wicri:regionArea>Department of Dermatology, Hospital del Mar, Institut Hospital del Mar d'Investigacions Mèdiques, Barcelona</wicri:regionArea>
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<name sortKey="Hertl, Michael" sort="Hertl, Michael" uniqKey="Hertl M" first="Michael" last="Hertl">Michael Hertl</name>
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<nlm:affiliation>Department of Dermatology, University Hospital, Marburg, Germany.</nlm:affiliation>
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<wicri:regionArea>Department of Dermatology, University Hospital, Marburg</wicri:regionArea>
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<name sortKey="Joly, Pascal" sort="Joly, Pascal" uniqKey="Joly P" first="Pascal" last="Joly">Pascal Joly</name>
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<nlm:affiliation>Clinique Dermatologique, Institut National de la Sante et de la Recherche Medicale (INSERM), INSERM U905, Rouen University Hospital, University of Rouen, Rouen, France; Dermatology Department, Rouen University Hospital, University of Rouen, Rouen, France.</nlm:affiliation>
<country xml:lang="fr">France</country>
<wicri:regionArea>Clinique Dermatologique, Institut National de la Sante et de la Recherche Medicale (INSERM), INSERM U905, Rouen University Hospital, University of Rouen, Rouen, France; Dermatology Department, Rouen University Hospital, University of Rouen, Rouen</wicri:regionArea>
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<region type="region">Région Normandie</region>
<region type="old region">Haute-Normandie</region>
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<author>
<name sortKey="Karpati, Sarolta" sort="Karpati, Sarolta" uniqKey="Karpati S" first="Sarolta" last="Karpati">Sarolta Karpati</name>
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<nlm:affiliation>Department of Dermatology, Venereology, and Dermatooncology of the Semmelweis University, Budapest, Hungary.</nlm:affiliation>
<country xml:lang="fr">Hongrie</country>
<wicri:regionArea>Department of Dermatology, Venereology, and Dermatooncology of the Semmelweis University, Budapest</wicri:regionArea>
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<settlement type="city">Budapest</settlement>
<region nuts="2">Hongrie centrale</region>
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<author>
<name sortKey="Kim, Jaehwan" sort="Kim, Jaehwan" uniqKey="Kim J" first="Jaehwan" last="Kim">Jaehwan Kim</name>
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<nlm:affiliation>Department of Dermatology at St George Hospital, University of New South Wales, Sydney, Australia; Laboratory for Investigative Dermatology, Rockefeller University, New York, New York.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">État de New York</region>
</placeName>
<wicri:cityArea>Department of Dermatology at St George Hospital, University of New South Wales, Sydney, Australia; Laboratory for Investigative Dermatology, Rockefeller University, New York</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Chan Kim, Soo" sort="Chan Kim, Soo" uniqKey="Chan Kim S" first="Soo" last="Chan Kim">Soo Chan Kim</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology and Cutaneous Biology Research Institute, Yonsei University College of Medicine, Gangnam Severance Hospital, Seoul, Korea.</nlm:affiliation>
<country xml:lang="fr">Corée du Sud</country>
<wicri:regionArea>Department of Dermatology and Cutaneous Biology Research Institute, Yonsei University College of Medicine, Gangnam Severance Hospital, Seoul</wicri:regionArea>
<placeName>
<settlement type="city">Séoul</settlement>
<region type="capital">Région capitale de Séoul</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Korman, Neil J" sort="Korman, Neil J" uniqKey="Korman N" first="Neil J" last="Korman">Neil J. Korman</name>
<affiliation wicri:level="2">
<nlm:affiliation>Department of Dermatology and the Murdough Family Center for Psoriasis, University Hospitals Case Medical Center, Cleveland, Ohio.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Ohio</region>
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<wicri:cityArea>Department of Dermatology and the Murdough Family Center for Psoriasis, University Hospitals Case Medical Center, Cleveland</wicri:cityArea>
</affiliation>
</author>
<author>
<name sortKey="Kowalewski, Cezary" sort="Kowalewski, Cezary" uniqKey="Kowalewski C" first="Cezary" last="Kowalewski">Cezary Kowalewski</name>
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<nlm:affiliation>Department of Dermatology and Immunodermatology, Medical University of Warsaw, Warsaw, Poland.</nlm:affiliation>
<country xml:lang="fr">Pologne</country>
<wicri:regionArea>Department of Dermatology and Immunodermatology, Medical University of Warsaw, Warsaw</wicri:regionArea>
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<author>
<name sortKey="Lee, Sang Eun" sort="Lee, Sang Eun" uniqKey="Lee S" first="Sang Eun" last="Lee">Sang Eun Lee</name>
<affiliation wicri:level="1">
<nlm:affiliation>Department of Dermatology, CHA Bundang Medical Center, CHA University, Seongnam, Korea.</nlm:affiliation>
<country xml:lang="fr">Corée du Sud</country>
<wicri:regionArea>Department of Dermatology, CHA Bundang Medical Center, CHA University, Seongnam</wicri:regionArea>
<wicri:noRegion>Seongnam</wicri:noRegion>
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<author>
<name sortKey="Rubenstein, David R" sort="Rubenstein, David R" uniqKey="Rubenstein D" first="David R" last="Rubenstein">David R. Rubenstein</name>
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<nlm:affiliation>Department of Dermatology, University of North Carolina at Chapel Hill, Chapel Hill, North Carolina.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
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<region type="state">Caroline du Nord</region>
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<wicri:cityArea>Department of Dermatology, University of North Carolina at Chapel Hill, Chapel Hill</wicri:cityArea>
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<name sortKey="Sprecher, Eli" sort="Sprecher, Eli" uniqKey="Sprecher E" first="Eli" last="Sprecher">Eli Sprecher</name>
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<nlm:affiliation>Department of Dermatology, Tel Aviv Sourasky Medical Center, Tel Aviv, Israel.</nlm:affiliation>
<country xml:lang="fr">Israël</country>
<wicri:regionArea>Department of Dermatology, Tel Aviv Sourasky Medical Center, Tel Aviv</wicri:regionArea>
<wicri:noRegion>Tel Aviv</wicri:noRegion>
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<name sortKey="Yancey, Kim" sort="Yancey, Kim" uniqKey="Yancey K" first="Kim" last="Yancey">Kim Yancey</name>
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<nlm:affiliation>Department of Dermatology, University of Texas Southwestern Medical Center, Dallas, Texas.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Texas</region>
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<wicri:cityArea>Department of Dermatology, University of Texas Southwestern Medical Center, Dallas</wicri:cityArea>
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<author>
<name sortKey="Zambruno, Giovanna" sort="Zambruno, Giovanna" uniqKey="Zambruno G" first="Giovanna" last="Zambruno">Giovanna Zambruno</name>
<affiliation wicri:level="3">
<nlm:affiliation>Laboratory of Molecular and Cell Biology, Istituto Dermopatico dell'Immacolata, IRCCS, Rome, Italy.</nlm:affiliation>
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Laboratory of Molecular and Cell Biology, Istituto Dermopatico dell'Immacolata, IRCCS, Rome</wicri:regionArea>
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<settlement type="city">Rome</settlement>
<region nuts="2">Latium</region>
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<name sortKey="Zillikens, Detlef" sort="Zillikens, Detlef" uniqKey="Zillikens D" first="Detlef" last="Zillikens">Detlef Zillikens</name>
<affiliation wicri:level="1">
<nlm:affiliation>Department of Dermatology, University of Lubeck, Lubeck, Germany.</nlm:affiliation>
<country xml:lang="fr">Allemagne</country>
<wicri:regionArea>Department of Dermatology, University of Lubeck, Lubeck</wicri:regionArea>
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<wicri:noRegion>Lubeck</wicri:noRegion>
<wicri:noRegion>Lubeck</wicri:noRegion>
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<name sortKey="Doan, Serge" sort="Doan, Serge" uniqKey="Doan S" first="Serge" last="Doan">Serge Doan</name>
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<nlm:affiliation>Department of Ophthalmology, Hopital Bichat, Paris, France; Fondation A de Rothschild, Paris, France.</nlm:affiliation>
<country xml:lang="fr">France</country>
<wicri:regionArea>Department of Ophthalmology, Hopital Bichat, Paris, France; Fondation A de Rothschild, Paris</wicri:regionArea>
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<region type="region">Île-de-France</region>
<region type="old region">Île-de-France</region>
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<name sortKey="Daniel, Benjamin S" sort="Daniel, Benjamin S" uniqKey="Daniel B" first="Benjamin S" last="Daniel">Benjamin S. Daniel</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Dermatology at St George Hospital, University of New South Wales, Sydney, Australia.</nlm:affiliation>
<country xml:lang="fr">Australie</country>
<wicri:regionArea>Department of Dermatology at St George Hospital, University of New South Wales, Sydney</wicri:regionArea>
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<region type="état">Nouvelle-Galles du Sud</region>
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<name sortKey="Werth, Victoria P" sort="Werth, Victoria P" uniqKey="Werth V" first="Victoria P" last="Werth">Victoria P. Werth</name>
<affiliation wicri:level="2">
<nlm:affiliation>Philadelphia Department of Veterans Affairs Medical Center, University of Pennsylvania, Philadelphia, Pennsylvania; Department of Dermatology, University of Pennsylvania, Philadelphia, Pennsylvania.</nlm:affiliation>
<country xml:lang="fr">États-Unis</country>
<placeName>
<region type="state">Pennsylvanie</region>
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<wicri:cityArea>Philadelphia Department of Veterans Affairs Medical Center, University of Pennsylvania, Philadelphia, Pennsylvania; Department of Dermatology, University of Pennsylvania, Philadelphia</wicri:cityArea>
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<series>
<title level="j">Journal of the American Academy of Dermatology</title>
<idno type="eISSN">1097-6787</idno>
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<date when="2015" type="published">2015</date>
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<keywords scheme="KwdEn" xml:lang="en">
<term>Humans</term>
<term>Pemphigoid, Benign Mucous Membrane (diagnosis)</term>
<term>Pemphigoid, Benign Mucous Membrane (therapy)</term>
<term>Practice Guidelines as Topic</term>
<term>Records as Topic</term>
<term>Treatment Outcome</term>
</keywords>
<keywords scheme="KwdFr" xml:lang="fr">
<term>Documents comme sujet</term>
<term>Guides de bonnes pratiques cliniques comme sujet</term>
<term>Humains</term>
<term>Pemphigoïde bénigne des muqueuses ()</term>
<term>Pemphigoïde bénigne des muqueuses (diagnostic)</term>
<term>Résultat thérapeutique</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en">
<term>Pemphigoid, Benign Mucous Membrane</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnostic" xml:lang="fr">
<term>Pemphigoïde bénigne des muqueuses</term>
</keywords>
<keywords scheme="MESH" qualifier="therapy" xml:lang="en">
<term>Pemphigoid, Benign Mucous Membrane</term>
</keywords>
<keywords scheme="MESH" xml:lang="en">
<term>Humans</term>
<term>Practice Guidelines as Topic</term>
<term>Records as Topic</term>
<term>Treatment Outcome</term>
</keywords>
<keywords scheme="MESH" xml:lang="fr">
<term>Documents comme sujet</term>
<term>Guides de bonnes pratiques cliniques comme sujet</term>
<term>Humains</term>
<term>Pemphigoïde bénigne des muqueuses</term>
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<front>
<div type="abstract" xml:lang="en">Mucous membrane pemphigoid encompasses a group of autoimmune bullous diseases with a similar phenotype characterized by subepithelial blisters, erosions, and scarring of mucous membranes, skin, or both. Although knowledge about autoimmune bullous disease is increasing, there is often a lack of clear definitions of disease, outcome measures, and therapeutic end points. With clearer definitions and outcome measures, it is possible to directly compare the results and data from various studies using meta-analyses. This consensus statement provides accurate and reproducible definitions for disease extent, activity, outcome measures, end points, and therapeutic response for mucous membrane pemphigoid and proposes a disease extent score, the Mucous Membrane Pemphigoid Disease Area Index.</div>
</front>
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<name sortKey="Herrero Gonzalez, Josep E" sort="Herrero Gonzalez, Josep E" uniqKey="Herrero Gonzalez J" first="Josep E" last="Herrero-González">Josep E. Herrero-González</name>
</region>
</country>
<country name="Hongrie">
<region name="Hongrie centrale">
<name sortKey="Karpati, Sarolta" sort="Karpati, Sarolta" uniqKey="Karpati S" first="Sarolta" last="Karpati">Sarolta Karpati</name>
</region>
</country>
<country name="Corée du Sud">
<region name="Région capitale de Séoul">
<name sortKey="Chan Kim, Soo" sort="Chan Kim, Soo" uniqKey="Chan Kim S" first="Soo" last="Chan Kim">Soo Chan Kim</name>
</region>
<name sortKey="Lee, Sang Eun" sort="Lee, Sang Eun" uniqKey="Lee S" first="Sang Eun" last="Lee">Sang Eun Lee</name>
</country>
<country name="Israël">
<noRegion>
<name sortKey="Sprecher, Eli" sort="Sprecher, Eli" uniqKey="Sprecher E" first="Eli" last="Sprecher">Eli Sprecher</name>
</noRegion>
</country>
</tree>
</affiliations>
</record>

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